kuvan
biomarin international limited - sapropterin dihydrochloride - fenilketonurije - drugi zdravljene bolezni prebavil in presnove izdelki, - kuvan je indiciran za zdravljenje hiperfenilalaninemije (hpa) pri odraslih in pediatričnih bolnikih vseh starosti s fenilketonurijo (pku), za katere se je izkazalo, da so odzivne na takšno zdravljenje. kuvan je tudi primerna za zdravljenje hyperphenylalaninaemia (hpa) pri odraslih in pediatričnih bolnikih vseh starosti z tetrahydrobiopterin (bh4) pomanjkljivosti, ki so pokazale, da se je treba odzivati na tako zdravljenje.
sapropterin dipharma
dipharma arzneimittel gmbh - sapropterin dihydrochloride - fenilketonurije - drugi zdravljene bolezni prebavil in presnove izdelki, - sapropterin dipharma is indicated for the treatment of hyperphenylalaninaemia (hpa) in adults and paediatric patients of all ages with phenylketonuria (pku) who have been shown to be responsive to such treatment. sapropterin dipharma is also indicated for the treatment of hyperphenylalaninaemia (hpa) in adults and paediatric patients of all ages with tetrahydrobiopterin (bh4) deficiency who have been shown to be responsive to such treatment.
aminosteril n-hepa 80 mg/ml raztopina za infundiranje
medias international d.o.o. - glicin; histidin; alanin; arginin; cistein; fenilalanin; izolevcin; levcin; lizin; metionin; prolin; serin; treonin; triptofan; valin - raztopina za infundiranje - glicin 2,91 g / 1 ml histidin1,4 g / 1 ml alanin2,32 g / 1 ml arginin5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; histidin 1,4 g / 1 ml alanin2,32 g / 1 ml arginin5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; alanin 2,32 g / 1 ml arginin5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; arginin 5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; cistein 0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; fenilalanin 0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml val - aminokisline
aminosteril n-hepa 80 mg/ml raztopina za infundiranje
medias international d.o.o. - glicin; histidin; alanin; arginin; cistein; fenilalanin; izolevcin; levcin; lizin; metionin; prolin; serin; treonin; triptofan; valin - raztopina za infundiranje - glicin 2,91 g / 1 ml histidin1,4 g / 1 ml alanin2,32 g / 1 ml arginin5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; histidin 1,4 g / 1 ml alanin2,32 g / 1 ml arginin5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; alanin 2,32 g / 1 ml arginin5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; arginin 5,36 g / 1 ml cistein0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; cistein 0,26 g / 1 ml fenilalanin0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml valin5,04 g / 1 ml; fenilalanin 0,44 g / 1 ml izolevcin5,2 g / 1 ml levcin6,55 g / 1 ml lizin3,44 g / 1 ml metionin0,55 g / 1 ml prolin2,87 g / 1 ml serin1,12 g / 1 ml treonin2,2 g / 1 ml triptofan0,35 g / 1 ml val - aminokisline
pku 1- mix z lcp milupanom prašek 450g
prašek za peroralno raztopino - hranila brez fenilalanina
pku 3 tempora vrečka 45 g 10x
hranila brez vsebnosti fenilalanina - prašek za peroralno raztopino - hranila brez vsebnosti fenilalanina 45 g / 1 vrečica - hranila brez fenilalanina
xphe for 2 660 g vrečka 33 g 20x
hranila brez vsebnosti fenilalanina - prašek za peroralno raztopino - hranila brez vsebnosti fenilalanina 33 g / 1 vrečica - hranila brez fenilalanina
xphe hello sadne ploščice, okus borovnic, ploščica 40 g 30x
farmacevtska oblika nedoločena - hranila brez fenilalanina