A16AX03 - search results

European Union - English - EMA (European Medicines Agency)

pheburane

eurocept international b. v. - sodium phenylbutyrate - carbamoyl-phosphate synthase i deficiency disease - various alimentary tract and metabolism products - treatment of chronic management of urea-cycle disorders.

Canada - English - Health Canada

pheburane granules

medunik canada - sodium phenylbutyrate - granules - 483mg - sodium phenylbutyrate 483mg

Israel - English - Ministry of Health

pheburane

truemed ltd, israel - sodium phenylbutyrate - granules - sodium phenylbutyrate 483 mg/g - sodium phenylbutyrate - pheburane is indicated as adjunctive therapy in the chronic management of urea cycle disorders, involving deficiencies of carbamylphosphate synthetase, ornithine transcarbamylase or argininosuccinate synthetase. it is indicated in all patients with neonatal-onset presentation (complete enzyme deficiencies, presenting within the first 28 days of life). it is also indicated in patients with late-onset disease (partial enzyme deficiencies, presenting after the first month of life) who have a history of hyperammonaemic encephalopathy.

European Union - English - EMA (European Medicines Agency)

ammonaps

immedica pharma ab - sodium phenylbutyrate - ornithine carbamoyltransferase deficiency disease; citrullinemia; carbamoyl-phosphate synthase i deficiency disease - other alimentary tract and metabolism products, - ammonaps is indicated as adjunctive therapy in the chronic management of urea cycle disorders, involving deficiencies of carbamylphosphate synthetase, ornithine transcarbamylase orargininosuccinate synthetase.it is indicated in all patients with neonatal-onset presentation (complete enzyme deficiencies, presenting within the first 28 days of life). it is also indicated in patients with late-onset disease(partial enzyme deficiencies, presenting after the first month of life) who have a history of hyperammonaemic encephalopathy.